[1]刘东辉 申慧鑫 李桂林 黄小钦.表现为脑干充血的颅-颈交界区硬脊膜动静脉瘘的临床及预后分析[J].卒中与神经疾病杂志,2021,28(03):338-341.[doi:10.3969/j.issn.1007-0478.2021.03.016]
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表现为脑干充血的颅-颈交界区硬脊膜动静脉瘘的临床及预后分析()
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《卒中与神经疾病》杂志[ISSN:1007-0478/CN:42-1402/R]

卷:
第28卷
期数:
2021年03期
页码:
338-341
栏目:
论著
出版日期:
2021-06-25

文章信息/Info

文章编号:
1007-0478(2021)03-0338-04
作者:
刘东辉 申慧鑫 李桂林 黄小钦
作者单位:100053 北京,首都医科大学宣武医院康复医学科(刘东辉),神经内科[申慧鑫 黄小钦(通信作者)],神经外科(李桂林)
分类号:
R743.4
DOI:
10.3969/j.issn.1007-0478.2021.03.016
文献标志码:
A
摘要:
目的 分析延-颈交界区硬脊膜动静脉瘘(Spinal dural arteriovenous fistulas, SDAVF)的临床、影像学特点,以提高临床医生对延-颈交界区SDAVF的认识和诊断水平。方法 回顾性分析7例表现为脑干充血的硬脊膜动静脉瘘患者的临床特点、影像学资料。结果 7例患者均为男性,平均年龄57.4岁; 急性起病4例,慢性进展性2例; 主要症状包括肢体无力(5例)、头晕(3例)、行走不稳(1例)、感觉障碍(3例)、构音障碍(1例)、顽固性呃逆(1例)、呼吸困难(1例)、颈部疼痛(1例)、大小便障碍(1例); 核磁共振成像(Magnetic resonance imaging,MRI)显示脑干受累部位主要在延髓,可见延髓增粗和髓内异常信号灶,脊髓周围有迂曲、虫蚀样血管流空影; 数字减影血管造影(Digital subtract angiography,DSA)显示脊髓引流静脉迂曲扩张,向上(4例)或向下(3例)引流,瘘口位于颅-颈交界区水平; 所有患者接受手术治疗后症状改善。结论 颅-颈交界区SDAVF可表现为脑干功能障碍,临床表现无特异性,易误诊; MRI可作为初步诊断方法,选择性脊髓血管造影是确诊的金标准; 及早治疗可逆转神经功能障碍。

参考文献/References:

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备注/Memo

备注/Memo:
基金项目:国家重点研发计划(2016YF0901004/2016YFC1300600); 首都医科大学基础临床科研合作课题(17JL-02,2016-2019)
更新日期/Last Update: 2021-06-25