[1]刘娟丽,杜宝琦,王丽.原发性胼胝体变性2例及文献复习[J].卒中与神经疾病杂志,2017,24(01):56-58+64.[doi:10.3969/j.issn.1007-0478.2017.01.015]
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原发性胼胝体变性2例及文献复习()
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《卒中与神经疾病》杂志[ISSN:1007-0478/CN:42-1402/R]

卷:
第24卷
期数:
2017年01期
页码:
56-58+64
栏目:
论 著
出版日期:
2017-02-26

文章信息/Info

文章编号:
1007-0478(2017)01-0056-04
作者:
刘娟丽杜宝琦王丽
725000 陕西省安康市人民医院神经内科; 山东省淄博市张店区人民医院神经内科(杜宝琦); 沈阳军区总医院神经内科(王丽(通信作者)
关键词:
原发性胼胝体变性 酒精中毒
分类号:
R744.5
DOI:
10.3969/j.issn.1007-0478.2017.01.015
摘要:
目的 探讨原发性胼胝体变性(Marchiafava-Bignami Disease,MBD)的临床及影像学特点。方法 分析本院诊治的2例原发性胼胝体变性患者的临床及影像学资料。结果 2例患者均有长期大量酗酒史,急性发病,出现神经系统症状,颅脑MRI出现特异性改变。2例给予大剂量维生素B1、甲钴胺肌肉注射,改善循环,例2给予地塞米松静滴后症状明显好转。结论 原发性胼胝体变性临床罕见,临床症状无特异性,若得不到及时诊治可发生不良后果,及时作出诊断、治疗可减少致残和致死率。

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更新日期/Last Update: 2017-02-20